{"id":24442,"date":"2009-07-23T00:28:47","date_gmt":"2005-04-09T15:47:54","guid":{"rendered":"http:\/\/www.tbeeb.net\/test\/%d8%a7%d9%84%d8%a3%d8%b3%d8%a7%d8%b3\/%d9%85%d8%b1%d8%b6-duchenne-muscular-dystrophy\/"},"modified":"2020-08-25T20:37:57","modified_gmt":"2020-08-25T17:37:57","slug":"%d9%85%d8%b1%d8%b6-duchenne-muscular-dystrophy","status":"publish","type":"post","link":"https:\/\/www.tbeeb.net\/health\/%d9%85%d8%b1%d8%b6-duchenne-muscular-dystrophy\/","title":{"rendered":"\u0645\u0631\u0636 \u062d\u062b\u0644 \u0639\u0636\u0644\u064a \u062f\u0648\u0634\u064a\u0646\u064a Duchenne Muscular Dystrophy"},"content":{"rendered":"<p><!--more--><span class=\"postbody\"><span style=\"font-weight: bold;\"><span style=\"font-size: 18px; line-height: normal;\"><br \/>\n\u00b7 \u0645\u0631\u0636 Duchenne Muscular Dystrophy<br \/>\n\u0627\u0644\u062a\u0639\u0631\u064a\u0641 Definition: \u0645\u0648 \u0645\u0631\u0636 \u0648\u0631\u0627\u062b\u064a \u064a\u062a\u0635\u0641 \u0628\u0633\u0631\u0639\u0629 \u062a\u062f\u0647\u0648\u0631 \u0648 \u0636\u0639\u0641 \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0648 \u0636\u0645\u0648\u0631\u0647\u0627 \u0648 \u0627\u0644\u062a\u064a \u062a\u0628\u062f\u0623 \u0645\u0646 \u0623\u0633\u0641\u0644 \u0627\u0644\u062c\u0633\u0645 (\u0627\u0644\u0642\u062f\u0645\u064a\u0646 \u062b\u0645 \u0627\u0644\u0631\u062c\u0644\u064a\u0646 \u062b\u0645 \u0627\u0644\u062d\u0648\u0636) \u0625\u0644\u0649 \u0623\u0639\u0644\u064a \u0644\u062a\u0634\u0645\u0644 \u0639\u0636\u0644\u0627\u062a \u0627\u0644\u062c\u0633\u0645 \u0643\u0644\u0647.<\/p>\n<p>\u00b7 \u0633\u0628\u0628 \u062d\u062f\u0648\u062b \u0627\u0644\u0645\u0631\u0636 Causes of Disease:<br \/>\n\u0627\u0644\u0648\u0631\u0627\u062b\u0629 Hereditary.. \u0628\u0633\u0628\u0628 \u062e\u0644\u0644 \u062c\u064a\u0646\u064a \u064a\u0633\u0628\u0628 \u062e\u0644\u0644 \u0641\u064a \u0639\u0645\u0644 \u0648\u0648\u0638\u064a\u0641\u0629 \u0648 \u062a\u0637\u0648\u0631 \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0628\u0633\u0628\u0628 \u0628\u0631\u0648\u062a\u064a\u0646 \u0628\u0633\u0645\u0649 \u062f\u064a\u0633\u062a\u0631\u0648\u0641\u064a\u0646 (dystrophin) \u064a\u0648\u062c\u062f \u0641\u064a \u0627\u0644\u0639\u0636\u0644\u0627\u062a.<br \/>\n\u00b7 \u0641\u062a\u0631\u0629 \u062d\u062f\u0648\u062b \u0627\u0644\u0645\u0631\u0636 Incidence period:<br \/>\n\u062a\u0638\u0647\u0631 \u0623\u0639\u0631\u0627\u0636 \u0627\u0644\u0645\u0631\u0636 \u0628\u0627\u0644\u0638\u0647\u0648\u0631 \u0642\u0628\u0644 \u0633\u0646 6 \u0633\u0646\u0648\u0627\u062a \u0648 \u064a\u0645\u0643\u0646 \u0623\u0646 \u062a\u0638\u0647\u0631 \u0641\u064a \u0627\u0644\u0633\u0646\u0629 \u0627\u0644\u0623\u0648\u0644\u0649.<br \/>\n\u0648 \u064a\u0635\u064a\u0628 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 2 \u0645\u0646 \u0643\u0644 10,000 \u0634\u062e\u0635.<\/p>\n<p>\u00b7 \u0645\u0631\u0627\u062d\u0644 \u062a\u0637\u0648\u0631 \u0627\u0644\u0645\u0631\u0636 Progress Phases:<br \/>\n\u0623\u0648\u0644 \u062a\u0638\u0647\u0631 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0639\u0644\u0649 \u0627\u0644\u0623\u0637\u0631\u0627\u0641 \u0627\u0644\u0633\u0641\u0644\u064a\u0629 \u062b\u0645 \u062a\u064a\u062f\u0623 \u0628\u0627\u0644\u0635\u0639\u0648\u062f \u0644\u0623\u0639\u0644\u0649 \u062b\u0645 \u062a\u0634\u0645\u0644 \u0639\u0636\u0644\u0627\u062a \u0627\u0644\u062c\u0633\u0643 \u0643\u0644\u0647 , \u0648 \u064a\u0644\u0627\u062d\u0638 \u0641\u064a \u0627\u0644\u0643\u062b\u064a\u0631 \u0645\u0646 \u0627\u0644\u062d\u0627\u0644\u0627\u062a \u062a\u0636\u062e\u0645 \u0639\u0636\u0644\u0629 \u0628\u0637\u0629 \u0627\u0644\u0631\u062c\u0644 Calf m.s..\u0648 \u0630\u0644\u0643 \u0646\u062a\u064a\u062c\u0629 \u0644\u062a\u062d\u0648\u0644 \u0627\u0644\u0623\u0646\u0633\u0633\u062c\u0629 \u0627\u0644\u0636\u0627\u0645\u0629 Connective tissues \u0625\u0644\u0649 \u0623\u0646\u0633\u062c\u0629 \u062f\u0647\u0646\u064a\u0629 Fat tissues \u0641\u064a\u0645\u0627 \u064a\u0639\u0631\u0641 \u0628\u0627\u0633\u0645 pseudohypertrophy \u0627\u0646\u062a\u0641\u0627\u062e \u0648 \u0646\u0645\u0648 \u0627\u0644\u0639\u0636\u0644\u0629 \u0627\u0644\u0643\u0627\u0630\u0628.<br \/>\n\u0648 \u064a\u0635\u064a\u0628 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 2 \u0645\u0646 \u0643\u0644 10,000 \u0634\u062e\u0635.<\/p>\n<p>\u064a\u062c\u0628 \u0623\u0646 \u0646\u0644\u0627\u062d\u0638 \u0627\u0644\u0641\u0631\u0642 \u0628\u064a\u0646 \u0647\u0630\u0627 \u0627\u0644\u0645\u0631\u0636 \u0648 \u0627\u0644\u0645\u0631\u0636 \u0627\u0644\u0630\u064a \u064a\u0633\u0645\u0649 Becker muscular dystrophy\u0648 \u0647\u0648 \u0645\u0634\u0627\u0628\u0647 \u0644\u0644\u0645\u0631\u0636 Duchenne muscular dystrophy \u0648 \u0644\u0643\u0646 \u0627\u0644\u0641\u0631\u0642 \u0628\u064a\u0646\u0647\u0645\u0627 \u064a\u0643\u0645\u0646 \u0641\u064a \u0627\u0644\u0628\u0637\u0621 \u0627\u0644\u0634\u062f\u064a\u062f \u0641\u064a \u062d\u062f\u0648\u062b \u0627\u0644\u0636\u0645\u0648\u0631 \u0627\u0644\u0639\u0636\u0644\u064a.<\/p>\n<p>\u00b7 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 Symptoms:<br \/>\n\u0627\u0644\u0648\u0647\u0646 \u0648 \u0627\u0644\u0636\u0639\u0641 \u0627\u0644\u0639\u0636\u0644\u064a Muscle weakness<br \/>\n\u062a\u0637\u0648\u0631 \u0648 \u062a\u062f\u0647\u0648\u0631 \u0633\u0631\u064a\u0639 Rapidly progressive<br \/>\n\u0627\u0644\u0633\u0642\u0648\u0637 \u0645\u062a\u0643\u0631\u0631Frequent falls<br \/>\n\u0635\u0639\u0648\u0628\u0629 \u0627\u0644\u062d\u0631\u0643\u0629 \u0643\u0627\u0644\u062c\u0631\u064a \u0648 \u0627\u0644\u0642\u0641\u0632Difficulty with motor skills<br \/>\n\u062a\u062f\u0647\u0648\u0631 \u0648 \u0632\u064a\u0627\u062f\u0629 \u0635\u0639\u0648\u0628\u0629 \u0627\u0644\u0645\u0634\u064aProgressive difficulty walking<br \/>\n\u0639\u062f\u0645 \u0627\u0644\u0642\u062f\u0631\u0629 \u0639\u0644\u0649 \u0627\u0644\u0645\u0634\u064a \u0628\u0628\u0644\u0648\u063a \u0633\u0646 12 \u0633\u0646\u0629<br \/>\n\u0627\u0644\u062a\u0639\u0628 \u0648 \u0627\u0644\u0625\u0631\u0647\u0627\u0642 \u0627\u0644\u0634\u062f\u064a\u062f\u0646<br \/>\n\u0645\u062d\u062a\u0645\u0644 \u062d\u062f\u0648\u062b \u0627\u0644\u062a\u062e\u0644\u0641 \u0627\u0644\u0639\u0642\u0644\u064a<br \/>\n\u062e\u0644\u0644 \u0641\u064a \u0627\u0644\u0647\u064a\u0643\u0644 \u0627\u0644\u0639\u0638\u0645\u064a<br \/>\n\u062a\u0642\u0648\u0633 \u0627\u0644\u0639\u0645\u0648\u062f \u0627\u0644\u0641\u0642\u0631\u064a \u0648 \u0627\u0644\u0638\u0647\u0631 \u0648 \u0627\u0644\u0635\u062f\u0631(scoliosis)<br \/>\n\u062e\u0644\u0644 \u0641\u064a \u0627\u0644\u0639\u0636\u0644\u0627\u062a<br \/>\n\u0642\u0635\u0631 \u0627\u0644\u0623\u0637\u0631\u0627\u0641.<br \/>\n\u062a\u0636\u062e\u0645 \u0628\u0637\u0629 \u0627\u0644\u0631\u062c\u0644 \u0627\u0644\u0643\u0627\u0630\u0628 Pseudohypertrophy<br \/>\n\u00b7 \u0627\u0644\u0641\u062d\u0648\u0635\u0627\u062a \u0627\u0644\u0639\u0644\u0627\u0645\u0627\u062a Signs &amp; tests:<br \/>\n\u0627\u0644\u0641\u062d\u0635 \u0627\u0644\u0633\u0631\u064a\u0631\u064a \u0648 \u064a\u0638\u0647\u0631 \u0627\u0644\u062e\u0644\u0644 \u0641\u064a \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u0647\u064a\u0643\u0644\u064a \u0648 \u0627\u0644\u0639\u0636\u0644\u064a \u0648 \u0645\u0634\u0627\u0643\u0644 \u0641\u064a \u0639\u0636\u0644\u0627\u062a \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u062a\u0646\u0641\u0633\u064a.<br \/>\n\u062e\u0644\u0644 \u0641\u064a \u0639\u0636\u0644\u0629 \u0627\u0644\u0642\u0644\u0628 Cardiomyopathy \u0648 \u0627\u062d\u062a\u0642\u0627\u0646\u0647 \u0623\u062d\u064a\u0627\u062a\u0627\u064b congestiveheartfailure \u0623\u0648 \u0639\u062f\u0645 \u0627\u0646\u062a\u0638\u0627\u0645 \u0636\u0631\u0628\u0627\u062a \u0627\u0644\u0642\u0644\u0628 arrhythmias \u0627\u0648 \u0625\u0644\u062a\u0647\u0627\u0628\u0627\u062a \u0627\u0644\u062c\u0647\u0627\u0632 \u0627\u0644\u062a\u0646\u0641\u0633\u064a pneumonia.\u0648 \u0623\u064a\u0636\u0627\u064b \u0639\u062f\u0645 \u0627\u0644\u062a\u0648\u0627\u0632\u0646.<br \/>\n\u0627\u0631\u062a\u0641\u0627\u0639 \u0641\u064a \u0625\u0646\u0632\u064a\u0645\u0627\u062a \u0627\u0644\u0642\u0644\u0628 \u0648 \u0645\u0646\u0647\u0627serum CPK<br \/>\n\u062a\u062e\u0637\u064a\u0637 \u0644\u0643\u0647\u0631\u0628\u064a\u0629 \u0627\u0644\u0639\u0636\u0644\u0627\u062a EMG (electromyography)<br \/>\n\u0623\u062e\u062f \u0639\u0646\u064a\u0629 \u0645\u0646 \u0646\u0633\u064a\u062c \u0639\u0636\u0644\u064a muscle biopsy<br \/>\n\u0627\u0644\u0623\u0634\u0639\u0629 \u0627\u0644\u0633\u064a\u0646\u064a\u0629 X-Ray \u0644\u0644\u0635\u062f\u0631.<br \/>\n\u00b7\u0627\u0644\u0639\u0644\u0627\u062c Treatment:<br \/>\n\u0644\u0627 \u064a\u0648\u062c\u062f \u0639\u0644\u0627\u062c \u0644\u0644\u0645\u0631\u0636 \u0648 \u0644\u0643\u0646 \u064a\u0628\u0642\u0649 \u0627\u0644\u062a\u062f\u062e\u0644 \u0645\u0646 \u0627\u062c\u0644 \u0627\u0644\u062a\u062e\u0641\u064a\u0641 \u0645\u0646 \u0627\u0644\u0623\u0639\u0631\u0627\u0636 \u0648 \u0627\u0644\u0639\u0644\u0627\u0645\u0627\u062a \u0648 \u0645\u0646\u0639 \u062d\u062f\u0648\u062b \u0627\u0644\u0645\u0636\u0627\u0639\u0641\u0627\u062a \u0627\u0644\u0646\u0627\u062a\u062c\u0629 \u0639\u0646 \u0639\u062f\u0645 \u0627\u0644\u062d\u0631\u0643\u0629 \u0648 \u0627\u0644\u0646\u0634\u0627\u0637.<\/p>\n<p>\u00b7 \u062a\u0648\u0642\u0639\u0627\u062a \u0644\u0645\u0635\u064a\u0631 \u0627\u0644\u0645\u0631\u0636 Expectations &amp; prognosis:<br \/>\n\u064a\u0633\u062a\u0645\u0631 \u0627\u0644\u0648\u0647\u0646 \u0648 \u0636\u0639\u0641 \u0648 \u0627\u0646\u0643\u0645\u0627\u0634 \u0627\u0644\u0639\u0636\u0644\u0627\u062a \u0625\u0644\u0649 \u0623\u0646 \u064a\u062a\u0633\u0628\u0628 \u0630\u0644\u0643 \u0641\u064a \u0641\u0634\u0644 \u0639\u0645\u0644\u064a\u0629 \u0627\u0644\u062a\u0646\u0641\u0633 \u0648 \u063a\u0627\u0644\u0628\u0627\u064b \u0645\u0646 \u062a\u062d\u062f\u062b \u0627\u0644\u0648\u0641\u0627\u0629 \u0641\u064a \u0633\u0646 25 \u0633\u0646\u0629.<\/p>\n<p>\u00b7 \u0645\u0646\u0639 \u062d\u062f\u0648\u062b \u0627\u0644\u0645\u0631\u0636Prevention:<br \/>\n\u0645\u0646 \u062e\u0644\u0627\u0644 \u062a\u0623\u0643\u062f \u0627\u0644\u0632\u0648\u062c\u064a\u0646 \u0645\u0646 \u0648\u062c\u0648\u062f \u062e\u0644\u0644 \u062c\u064a\u0646\u064a \u0641\u064a \u0623\u062d\u062f \u0627\u0644\u0639\u0627\u0626\u0644\u0627\u062a \u0648 \u0623\u064a\u0636\u0627\u064b \u0627\u0644\u0641\u062d\u0635 \u0627\u0644\u062c\u064a\u0646\u064a \u0644\u0644\u062c\u0646\u064a\u0646 \u0623\u062b\u0646\u0627\u0621 \u0627\u0644\u062d\u0645\u0644.<\/p>\n<p>\u00b7 \u0625\u0639\u062f\u0627\u062f \u0627\u0644\u062d\u0643\u0628\u0645: \u0623\u062f\u0647\u0645 \u0623\u062d\u0645\u062f<br \/>\n\u00b7 \u0645\u0646\u062a\u062f\u064a\u0627\u062a \u0637\u0628\u064a\u0628 \u062f\u0648\u062a \u0643\u0648\u0645<\/span><\/span><\/span><\/p>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[71],"tags":[],"class_list":["post-24442","post","type-post","status-publish","format-standard","hentry","category-71"],"_links":{"self":[{"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/posts\/24442","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/comments?post=24442"}],"version-history":[{"count":1,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/posts\/24442\/revisions"}],"predecessor-version":[{"id":1672917,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/posts\/24442\/revisions\/1672917"}],"wp:attachment":[{"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/media?parent=24442"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/categories?post=24442"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.tbeeb.net\/health\/wp-json\/wp\/v2\/tags?post=24442"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}